Protein substitutes for phenylketonuria in Europe: access and nutritional composition

Pena M. J., de Almeida M. F., van Dam E., Ahring K., Belanger-Quintana A., Dokoupil K., ...More

EUROPEAN JOURNAL OF CLINICAL NUTRITION, vol.70, no.7, pp.785-789, 2016 (SCI-Expanded) identifier identifier identifier

  • Publication Type: Article / Article
  • Volume: 70 Issue: 7
  • Publication Date: 2016
  • Doi Number: 10.1038/ejcn.2016.54
  • Journal Name: EUROPEAN JOURNAL OF CLINICAL NUTRITION
  • Journal Indexes: Science Citation Index Expanded (SCI-EXPANDED), Scopus
  • Page Numbers: pp.785-789
  • Hacettepe University Affiliated: Yes

Abstract

BACKGROUND/OBJECTIVES: Protein substitutes (PS) are an essential component in the dietary management of phenylketonuria (PKU). PS are available as phenylalanine-free amino-acid mixtures (AAM), glycomacropeptide-based PS (GMP) and large neutral amino acids (LNAA). There is a lack of information regarding their availability in different countries and comparison of their nutritional composition is limited. The objectives of this study were to identify the number of PS available in different European countries and Turkey and to compare their nutritional composition.