Protein substitutes for phenylketonuria in Europe: access and nutritional composition


Pena M. J. , de Almeida M. F. , van Dam E., Ahring K., Belanger-Quintana A., Dokoupil K., ...Daha Fazla

EUROPEAN JOURNAL OF CLINICAL NUTRITION, cilt.70, ss.785-789, 2016 (SCI İndekslerine Giren Dergi) identifier identifier identifier

  • Cilt numarası: 70 Konu: 7
  • Basım Tarihi: 2016
  • Doi Numarası: 10.1038/ejcn.2016.54
  • Dergi Adı: EUROPEAN JOURNAL OF CLINICAL NUTRITION
  • Sayfa Sayıları: ss.785-789

Özet

BACKGROUND/OBJECTIVES: Protein substitutes (PS) are an essential component in the dietary management of phenylketonuria (PKU). PS are available as phenylalanine-free amino-acid mixtures (AAM), glycomacropeptide-based PS (GMP) and large neutral amino acids (LNAA). There is a lack of information regarding their availability in different countries and comparison of their nutritional composition is limited. The objectives of this study were to identify the number of PS available in different European countries and Turkey and to compare their nutritional composition.