Systematic review of childhood-onset polyarteritis nodosa and DADA2.

Kasap Cuceoglu M. , Sener S. , Batu E. D. , Kaya Akca U., Demir S., Sag E., ...More

Seminars in arthritis and rheumatism, vol.51, pp.559-564, 2021 (Journal Indexed in SCI) identifier identifier identifier

  • Publication Type: Article / Article
  • Volume: 51
  • Publication Date: 2021
  • Doi Number: 10.1016/j.semarthrit.2021.04.009
  • Title of Journal : Seminars in arthritis and rheumatism
  • Page Numbers: pp.559-564
  • Keywords: Polyarteritis nodosa, Deficiency of adenosine deaminase 2, Systematic review, Child, immunosuppressants, Biological therapies, Outcome measures, Vasculitis, ADENOSINE-DEAMINASE 2, PHENOTYPIC VARIABILITY, PEDIATRIC VASCULITIS, ADA2 DEFICIENCY, CASE SERIES, CHILDREN, DISEASE, MUTATIONS, GENOTYPE, CLASSIFICATION


Background: Diagnosis of childhood polyarteritis nodosa (PAN) has become challenging after the definition of deficiency of adenosine deaminase 2 (DADA2). We aimed to define the differential features of pediatric PAN and DADA2 patients in our center and in the literature.