Bidirectional Glenn shunt in an infant with prune-belly syndrome

Dogan R., Yilmaz M., Duman U., Ozkutlu S.

THORACIC AND CARDIOVASCULAR SURGEON, cilt.49, sa.6, ss.378-379, 2001 (SCI-Expanded, Scopus) identifier identifier identifier

  • Yayın Türü: Makale / Tam Makale
  • Cilt numarası: 49 Sayı: 6
  • Basım Tarihi: 2001
  • Doi Numarası: 10.1055/s-2001-19012
  • Dergi Adı: THORACIC AND CARDIOVASCULAR SURGEON
  • Derginin Tarandığı İndeksler: Science Citation Index Expanded (SCI-EXPANDED), Scopus
  • Sayfa Sayıları: ss.378-379
  • Anahtar Kelimeler: prune-belly syndrome, congenital heart disease, open heart surgery, Glenn procedure, ABNORMALITIES, DEFICIENCY
  • Hacettepe Üniversitesi Adresli: Evet

Özet

The prune-belly syndrome (PBS) usually is described as a deficiency of the anterior abdominal muscle involving bilateral cryptorchidism and urinary tract malformations. In this report, we will present an eleven-month-old boy with PBS associated with a complex cardiac anomaly. A bilateral bidirectional Glenn shunt was performed with the diagnosis of isolated clextrocardia, single ventricle, pulmonary atresia, incomplete A-V septal defect, hemiazygos continuity, persistent right superior vena cava, patent ductus arteriosus-dependent pulmonary blood flow. The patient required special consideration for postoperative pulmonary care.