Bidirectional Glenn shunt in an infant with prune-belly syndrome
THORACIC AND CARDIOVASCULAR SURGEON, vol.49, no.6, pp.378-379, 2001 (SCI-Expanded, Scopus)
- Publication Type: Article / Article
- Volume: 49 Issue: 6
- Publication Date: 2001
- Doi Number: 10.1055/s-2001-19012
- Journal Name: THORACIC AND CARDIOVASCULAR SURGEON
- Journal Indexes: Science Citation Index Expanded (SCI-EXPANDED), Scopus
- Page Numbers: pp.378-379
- Keywords: prune-belly syndrome, congenital heart disease, open heart surgery, Glenn procedure, ABNORMALITIES, DEFICIENCY
- Hacettepe University Affiliated: Yes
Abstract
The prune-belly syndrome (PBS) usually is described as a deficiency of the anterior abdominal muscle involving bilateral cryptorchidism and urinary tract malformations. In this report, we will present an eleven-month-old boy with PBS associated with a complex cardiac anomaly. A bilateral bidirectional Glenn shunt was performed with the diagnosis of isolated clextrocardia, single ventricle, pulmonary atresia, incomplete A-V septal defect, hemiazygos continuity, persistent right superior vena cava, patent ductus arteriosus-dependent pulmonary blood flow. The patient required special consideration for postoperative pulmonary care.