Akademik Veri Yönetim Sistemi
Cocuk Sagligi ve Hastaliklari Dergisi, cilt.60, sa.1, ss.1-6, 2017 (Scopus)
The increased skill and wide spread application of antenatal ultrasound has allowed precise early diagnosis of many congenital lung malformations including congenital pulmonary airway malformation, pulmonary sequestration, bronchogenic cyst and congenital lobar emphysema. Here we aimed to evaluate the clinical, radiological and laboratory findings of our patients with congenital lung malformations; also we aimed to compare prenatal and postnatal diagnosis of congenital lung malformations. The hospital files of patients in Hacettepe University Ihsan Dogramaci Children's Hospital, Pediatric Pulmonology Department with congenital lung malformations between January 2004-July 2014 have been evaluated for clinical, radiological and laboratory findings. We analyzed the clinical management of all patients. Also the differences between antenatal and postnatal diagnosis were documented. 80 patients with congenital lung malformations have been followed at our department in the last ten years. According to diagnosis, 35 patients (42.5%) with congenital pulmonary airway malformation, 26 patients (32.5%) with congenital lobar emphysema, five patients (6.3%) with pulmonary hypoplasia, seven (8.8%) patients with pulmonary sequestration, three patients (3.8%) with enteric cyst, one patient (1.3%) with thymic hemangioma, one patient (1.3%) with bronchogenic cyst, one patient (1.3%) with congenital pulmonary airway malformation and congenital lobar emphysema and one patient (1.3%) with bronchial atresia were detected. The most common radiological findings were lung cysts and pneumonic consolidation in congenital pulmonary airway malformation; hyperinflation with mediastinal shift in congenital lobar emphysema. From the 24 patients with antenatally diagnosed congenital pulmonary airway malformation, 16 patients with congenital pulmonary airway malformation, two patients with congenital lobar emphysema, one patient with pulmonary sequestration, two patients with enteric cyst, one patient with thymic hemangioma, one patient with small airway disease and one patient with bronchial atresia were diagnosed. Congenital lung malformations are a heterogenous group of disorders that can be diagnosed at early age with the new imaging modalities such as chest CT, prenatal ultrasound, CT angiography and magnetic resonance imaging. The clinical manifestation of these malformations varies from respiratory distress in the immediate postnatal period to an incidental finding on routine chest radiography. With early diagnosis and treatment, patients can get a better life for respiratory functions than expected.