Congenital hepatic fibrosis associated with cavernous transformation of the portal vein


BAYRAKTAR Y. , BALKANCI F. , KAYHAN B., UZUNALIMOGLU B., OZENC A., OZDEMIR A., ...More

HEPATO-GASTROENTEROLOGY, vol.44, no.18, pp.1588-1594, 1997 (Journal Indexed in SCI) identifier identifier identifier

  • Publication Type: Article / Article
  • Volume: 44 Issue: 18
  • Publication Date: 1997
  • Title of Journal : HEPATO-GASTROENTEROLOGY
  • Page Numbers: pp.1588-1594

Abstract

Background/Aims: Congenital hepatic fibrosis (CHF), which is one of the fibropolycystic diseases, occurs in various forms. Portal hypertension, a very common clinical feature of this condition, has been attributed to the compression of portal vein radicles in the fibrous bands. We investigated whether there are any other contributing factors in the development of portal hypertension in patients with CHF.