Pili annulati is a rare autosomal dominant inherited hair shaft disorder. It is characterized by alternating light and dark bands and there is no association with hair fragility. A 8-year-old girl presented to our dermatology outpatient clinic with a 7-year history of hair disorder. Dermatologic examination revealed light and dark banding of hairs. Light microscopy of the hairs displayed intermittent dark banding. Scanning electron microscopy revealed cavities within the cortex of hair. In the light of clinical and microscopic findings, the patient was diagnosed with pili annulati and to the best of our knowledge, our patient is the first case reported from Turkey.