Claude Syndrome in Childhood Associated with Probable Neuro-Behcet Disease

Yavuz P., SOLMAZ İ., Kaya U. A., Akgoz A., Oguz K. K., Aytac S., ...More

Neuropediatrics, vol.54, no.1, pp.82-87, 2023 (SCI-Expanded) identifier identifier identifier

  • Publication Type: Article / Article
  • Volume: 54 Issue: 1
  • Publication Date: 2023
  • Doi Number: 10.1055/s-0042-1759794
  • Journal Name: Neuropediatrics
  • Journal Indexes: Science Citation Index Expanded (SCI-EXPANDED), Scopus, Academic Search Premier, BIOSIS, EMBASE, MEDLINE
  • Page Numbers: pp.82-87
  • Keywords: Claude syndrome, oculomotor nerve palsy, hemiataxia, posterior stroke, neuro-Behcet disease
  • Hacettepe University Affiliated: Yes

Abstract

Thieme. All rights reserved.Claude syndrome is a rare midbrain stroke syndrome characterized by ipsilateral third cranial nerve palsy and contralateral hemiataxia. So far, only a few cases have been reported in childhood. We present two children with Claude syndrome at 9 and 15 years of age. The typical clinical picture was consistent with brain magnetic resonance imaging findings. A thorough investigation regarding the underlying etiology revealed no definite diagnosis but clues suggestive of probable neuro-Behcet disease. Awareness of pediatric neurologists on arterial ischemic stroke has been increasing over the past decades, enabling timely diagnosis and appropriate management of rare childhood cases with midbrain stroke.