Gangliogliomas are uncommon slow-growing benign tumors of the central nervous system. They are frequently localized in temporal lobes and frequently seen during childhood. Our case differs from the cases reported in literature in respect to localization, congenital landmarks and age of presentation. We should keep in mind that gangliogliomas can take place in the occipital lobe rarely, and in older ages. The patient in this report admitted to our hospital with a seizure, which is usual for gangliogiomas. He was older when compared to the ganglioglioma patients reported in the literature with some congenital abnormalities. Three years after gross-total resection, patient still does not have contrast agent enhancement in the control magnetic resonance imaging scans. Congenital malformations can be informative four gangliogliomas in the future if this case is supported by some others.