Towards a new set of classification criteria for PFAPA syndrome


Vanoni F., Caorsi R., Aeby S., Cochard M., Anton J., Berg S., ...More

PEDIATRIC RHEUMATOLOGY, vol.16, 2018 (SCI-Expanded) identifier identifier identifier

  • Publication Type: Article / Article
  • Volume: 16
  • Publication Date: 2018
  • Doi Number: 10.1186/s12969-018-0277-2
  • Journal Name: PEDIATRIC RHEUMATOLOGY
  • Journal Indexes: Science Citation Index Expanded (SCI-EXPANDED), Scopus
  • Hacettepe University Affiliated: Yes

Abstract

Background: Diagnosis of Periodic Fever, Aphthous stomatitis, Pharyngitis and Cervical Adenitis (PFAPA) syndrome is currently based on the modified Marshall's criteria, but no validated evidence based classification criteria for PFAPA has been established so far.