Clinical spectrum of children with interstitial pneumonia with autoimmune features

Tural D. A. , EMİRALİOĞLU N., Ozsezen B., SUNMAN B., Buyuksahin H. N. , GÜZELKAŞ İ., ...More

RESPIRATORY MEDICINE, vol.187, 2021 (Peer-Reviewed Journal) identifier identifier identifier

  • Publication Type: Article / Article
  • Volume: 187
  • Publication Date: 2021
  • Doi Number: 10.1016/j.rmed.2021.106566
  • Journal Indexes: Science Citation Index Expanded, Scopus, CAB Abstracts, EMBASE, MEDLINE, Pollution Abstracts
  • Keywords: Interstitial lung disease (ILD), Interstitial pneumonia with autoimmune features (IPAF), Connective tissue disease (CTD), Idiopathic interstitial pneumonia, LUNG-DISEASE, MANAGEMENT, THERAPY


Background: Interstitial pneumonia with autoimmune features (IPAF) is a term used to describe adult patients with interstitial lung disease (ILD) who display some clinical or serological features of autoimmune diseases and who do not meet the full criteria for a specific connective tissue disease (CTD). The aim of this study was to define the demographic, clinical, radiologic, serologic and histopathologic features and assess treatment in children with IPAF.