Enigmatic entity in childhood: clival chordoma from a tertiary center's perspective


BİLGİNER B. , Turk C. C. , Narin F., HANALİOĞLU Ş. , Oguz K. K. , ÖZGEN MOCAN B. , ...More

ACTA NEUROCHIRURGICA, vol.157, no.9, pp.1587-1593, 2015 (Journal Indexed in SCI) identifier identifier identifier

  • Publication Type: Article / Article
  • Volume: 157 Issue: 9
  • Publication Date: 2015
  • Doi Number: 10.1007/s00701-015-2510-9
  • Title of Journal : ACTA NEUROCHIRURGICA
  • Page Numbers: pp.1587-1593

Abstract

Chordoma is a rare neoplasm that arises from embryonic notochordal remnants along the axial skeleton (i.e., clivus, sacrum) and the vertebral bodies. They comprise less than 1 % of CNS tumors and 1-4 % of all bone malignancies. It rarely affects children and adolescents (< 5 %). Chordomas are locally aggressive and highly recurrent. Their management is challenging for clinicians.