Promising effect of intravenous immunoglobulin therapy for epidermolysis bullosa pruriginosa

Ertop P., Vural S., Ili E. G., Durmaz C. D., HEPER A., McGrath J. A., ...More

INTERNATIONAL JOURNAL OF DERMATOLOGY, vol.59, no.7, pp.851-855, 2020 (SCI-Expanded) identifier identifier identifier

  • Publication Type: Article / Article
  • Volume: 59 Issue: 7
  • Publication Date: 2020
  • Doi Number: 10.1111/ijd.14951
  • Journal Name: INTERNATIONAL JOURNAL OF DERMATOLOGY
  • Journal Indexes: Science Citation Index Expanded (SCI-EXPANDED), Scopus, Academic Search Premier, Agricultural & Environmental Science Database, CAB Abstracts, EMBASE, MEDLINE, Veterinary Science Database
  • Page Numbers: pp.851-855
  • Hacettepe University Affiliated: No

Abstract

Background Epidermolysis bullosa pruriginosa (EBP) is rare a clinical variant of dystrophic epidermolysis bullosa characterized by trauma-induced bullae formation, milia and nail dystrophy accompanied by severe pruritus. Treatment pruritus of EBP focuses on immunosuppressive treatment with limited efficacy. Treatment strategies are not well-established.