Promising effect of intravenous immunoglobulin therapy for epidermolysis bullosa pruriginosa
INTERNATIONAL JOURNAL OF DERMATOLOGY, cilt.59, sa.7, ss.851-855, 2020 (SCI-Expanded, Scopus)
- Yayın Türü: Makale / Tam Makale
- Cilt numarası: 59 Sayı: 7
- Basım Tarihi: 2020
- Doi Numarası: 10.1111/ijd.14951
- Dergi Adı: INTERNATIONAL JOURNAL OF DERMATOLOGY
- Derginin Tarandığı İndeksler: Science Citation Index Expanded (SCI-EXPANDED), Scopus, Academic Search Premier, Agricultural & Environmental Science Database, CAB Abstracts, EMBASE, MEDLINE, Veterinary Science Database
- Sayfa Sayıları: ss.851-855
- Hacettepe Üniversitesi Adresli: Hayır
Özet
Background Epidermolysis bullosa pruriginosa (EBP) is rare a clinical variant of dystrophic epidermolysis bullosa characterized by trauma-induced bullae formation, milia and nail dystrophy accompanied by severe pruritus. Treatment pruritus of EBP focuses on immunosuppressive treatment with limited efficacy. Treatment strategies are not well-established.