International Retrospective Chart Review of Treatment Patterns in Severe Familial Mediterranean Fever, Tumor Necrosis Factor Receptor-Associated Periodic Syndrome, and Mevalonate Kinase Deficiency/Hyperimmunoglobulinemia D Syndrome

ÖZEN S., Kuemmerle-Deschner J. B. , Cimaz R., Livneh A., Quartier P., Kone-Paut I., ...More

ARTHRITIS CARE & RESEARCH, vol.69, no.4, pp.578-586, 2017 (Peer-Reviewed Journal) identifier identifier identifier

  • Publication Type: Article / Article
  • Volume: 69 Issue: 4
  • Publication Date: 2017
  • Doi Number: 10.1002/acr.23120
  • Journal Indexes: Science Citation Index Expanded, Scopus
  • Page Numbers: pp.578-586


Objective. Periodic fever syndrome (PFS) conditions are characterized by recurrent attacks of fever and localized inflammation. This study examined the diagnostic pathway and treatments at tertiary centers for familial Mediterranean fever (FMF), tumor necrosis factor receptor-associated periodic syndrome (TRAPS), and mevalonate kinase deficiency (MKD)/hyperimmunoglobulinemia D syndrome (HIDS).