International management platform for children's interstitial lung disease (chILD-EU)


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Griese M., Seidl E., Hengst M., Reu S., Rock H., Anthony G., ...More

THORAX, vol.73, no.3, pp.231-239, 2018 (SCI-Expanded) identifier identifier identifier

  • Publication Type: Article / Article
  • Volume: 73 Issue: 3
  • Publication Date: 2018
  • Doi Number: 10.1136/thoraxjnl-2017-210519
  • Journal Name: THORAX
  • Journal Indexes: Science Citation Index Expanded (SCI-EXPANDED), Scopus
  • Page Numbers: pp.231-239
  • Keywords: paediatric interstitial lung disease, rare lung diseases, paediatric lung disaese, DIAGNOSIS, INFANCY, TRIALS
  • Hacettepe University Affiliated: Yes

Abstract

Background Children's interstitial lung diseases (chILD) cover many rare entities, frequently not diagnosed or studied in detail. There is a great need for specialised advice and for internationally agreed subclassification of entities collected in a register. Our objective was to implement an international management platform with independent multidisciplinary review of cases at presentation for long-term follow-up and to test if this would allow for more accurate diagnosis. Also, quality and reproducibility of a diagnostic subclassification system were assessed using a collection of 25 complex chILD cases.