International management platform for children's interstitial lung disease (chILD-EU)
THORAX, cilt.73, sa.3, ss.231-239, 2018 (SCI-Expanded, Scopus)
- Yayın Türü: Makale / Tam Makale
- Cilt numarası: 73 Sayı: 3
- Basım Tarihi: 2018
- Doi Numarası: 10.1136/thoraxjnl-2017-210519
- Dergi Adı: THORAX
- Derginin Tarandığı İndeksler: Science Citation Index Expanded (SCI-EXPANDED), Scopus
- Sayfa Sayıları: ss.231-239
- Anahtar Kelimeler: paediatric interstitial lung disease, rare lung diseases, paediatric lung disaese, DIAGNOSIS, INFANCY, TRIALS
- Açık Arşiv Koleksiyonu: AVESİS Açık Erişim Koleksiyonu
- Hacettepe Üniversitesi Adresli: Evet
Özet
Background Children's interstitial lung diseases (chILD) cover many rare entities, frequently not diagnosed or studied in detail. There is a great need for specialised advice and for internationally agreed subclassification of entities collected in a register. Our objective was to implement an international management platform with independent multidisciplinary review of cases at presentation for long-term follow-up and to test if this would allow for more accurate diagnosis. Also, quality and reproducibility of a diagnostic subclassification system were assessed using a collection of 25 complex chILD cases.