Primary Systemic Vasculitides as a Cause of Group IV Pulmonary Hypertension

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AKDOĞAN A., Sarı A., Sade L. E.

Anatolian Journal of Cardiology, cilt.27, ss.677-687, 2023 (SCI-Expanded) identifier identifier

  • Yayın Türü: Makale / Derleme
  • Cilt numarası: 27
  • Basım Tarihi: 2023
  • Doi Numarası: 10.14744/anatoljcardiol.2023.3650
  • Dergi Adı: Anatolian Journal of Cardiology
  • Derginin Tarandığı İndeksler: Science Citation Index Expanded (SCI-EXPANDED), Scopus, Academic Search Premier, CINAHL, EMBASE, MEDLINE, Directory of Open Access Journals, TR DİZİN (ULAKBİM)
  • Sayfa Sayıları: ss.677-687
  • Anahtar Kelimeler: Behçet’s disease, group IV PH, primary systemic vasculitides, Takayasu arteritis
  • Hacettepe Üniversitesi Adresli: Evet

Özet

The primary systemic vasculitides are rare diseases characterized by vessel wall inflammation. Isolated pulmonary vasculitis, large-vessel vasculitis, and Behçet’s disease are mimickers of chronic thromboembolic pulmonary hypertension (CTEPH); group IV pulmonary hypertension (PH) can occur as a devastating complication in the course of these diseases. Pulmonary endarterectomy, balloon angioplasty, anticoagulation and pulmonary vasodilator agents are the main treatment options for CTEPH. There is no specific recommendation for the treatment of patients having group IV PH due to primary systemic vasculitides. We reviewed herein data about group IV PH due to primary systemic vasculitides.