Congenital absence of the portal vein associated with congenital hepatic fibrosis

Gocmen R., Akhan O., Talim B.

PEDIATRIC RADIOLOGY, vol.37, no.9, pp.920-924, 2007 (SCI-Expanded) identifier identifier identifier

  • Publication Type: Article / Article
  • Volume: 37 Issue: 9
  • Publication Date: 2007
  • Doi Number: 10.1007/s00247-007-0533-y
  • Journal Name: PEDIATRIC RADIOLOGY
  • Journal Indexes: Science Citation Index Expanded (SCI-EXPANDED), Scopus
  • Page Numbers: pp.920-924
  • Hacettepe University Affiliated: Yes

Abstract

The radiological features of a 7-year-old boy with congenital absence of the portal vein, pathologically proven congenital hepatic fibrosis, double inferior vena cava, ventricular septal defect, vertebral anomalies, crossed fused renal ectopia, and facial anomalies with pathological correlation are reported. This association between congenital absence of the portal vein and congenital hepatic fibrosis is unique.