Primary amyloidosis presenting intrahepatic cholestasis and fulminant hepatic failure


Ates O. , KÖSEMEHMETOĞLU K. , Guner G. , Bayraktar Y.

ITALIAN JOURNAL OF MEDICINE, vol.10, no.1, pp.71-73, 2016 (Journal Indexed in ESCI) identifier identifier

  • Publication Type: Article / Article
  • Volume: 10 Issue: 1
  • Publication Date: 2016
  • Doi Number: 10.4081/itjm.2015.593
  • Title of Journal : ITALIAN JOURNAL OF MEDICINE
  • Page Numbers: pp.71-73

Abstract

A 69-year-old man noticed abdominal pain located on right upper quadrant. Physical examination showed hepatosplenomegaly and icteric discoloration of sclera. On evaluation, patient was diagnosed to have hepatic amyloidosis related monoclonal gammopathy of undetermined significance (MGUS) and sinusoidal obstruction syndrome with intrahepatic cholestasis. In this case report we emphasize fulminant hepatic failure due to primer amyloidosis in diagnosed with MGUS patient.