Factors associated with severe lung disease in an adult population with cystic fibrosis: a single center experience.

Er B. , Çelebioğlu E., Yalçin E., Doğru D., Erden A., Uzun Ö., ...More

Turkish journal of medical sciences, vol.50, pp.945-952, 2020 (Journal Indexed in SCI) identifier identifier identifier

  • Publication Type: Article / Article
  • Volume: 50
  • Publication Date: 2020
  • Doi Number: 10.3906/sag-1912-101
  • Title of Journal : Turkish journal of medical sciences
  • Page Numbers: pp.945-952
  • Keywords: Adult, cystic fibrosis, severe lung disease, risk factors, PULMONARY-FUNCTION, FEV1 DECLINE, CHILDREN, PROGRESSION, PREDICTORS, NUTRITION, MORTALITY, IVACAFTOR, ECFS


Background/Aim: The patients with cystic fibrosis (CF) are living longer compared to the past, but respiratory failure is still the most common cause of mortality. The aim of this study is to investigate factors associated with severe lung disease in a cohort of adult patients with CF.