JOURNAL OF AAPOS, vol.14, no.2, pp.175-177, 2010 (SCI-Expanded)
An 11-year-old boy presented with a mid-zonal pigment epithelial iris cyst. The cyst progressed relentlessly, ultimately leading to enucleation of the eye 4 years after presentation. Histopathology revealed a ciliary body schwannoma filling the anterior chamber and a small, incidental noncontiguous ciliary body melanoma. Vision loss, pupil distortion, and relentless growth despite complete cyst deflation following aspiration were clues for the tumor-induced nature of the visible cyst.