A preliminary score for the assessment of disease activity in hereditary recurrent fevers: results from the AIDAI (Auto-Inflammatory Diseases Activity Index) Consensus Conference

Piram, Maryam; Frenkel, Joost; Gattorno, Marco; ÖZEN, SEZA; Lachmann, Helen; Goldbach-Mansky, Raphaela; Hentgen, Veronique; Neven, Benedicte; Stojanovic, Katia; Simon, Anna; Kuemmerle-Deschner, Jasmin; Hoffman, Hal; Stojanov, Silvia; Duquesne, Agnes; Pillet, Pascal; Martini, Alberto; Pouchot, Jacques; Kone-Paut, Isabelle

doi:10.1136/ard.2010.132613

A preliminary score for the assessment of disease activity in hereditary recurrent fevers: results from the AIDAI (Auto-Inflammatory Diseases Activity Index) Consensus Conference

Piram M., Frenkel J., Gattorno M., ÖZEN S., Lachmann H. J., Goldbach-Mansky R., ...Daha Fazla

ANNALS OF THE RHEUMATIC DISEASES, cilt.70, sa.2, ss.309-314, 2011 (SCI-Expanded, Scopus)

Yayın Türü: Makale / Tam Makale
Cilt numarası: 70 Sayı: 2
Basım Tarihi: 2011
Doi Numarası: 10.1136/ard.2010.132613
Dergi Adı: ANNALS OF THE RHEUMATIC DISEASES
Derginin Tarandığı İndeksler: Science Citation Index Expanded (SCI-EXPANDED), Scopus
Sayfa Sayıları: ss.309-314
Açık Arşiv Koleksiyonu: AVESİS Açık Erişim Koleksiyonu
Hacettepe Üniversitesi Adresli: Evet

Özet

Background The systemic autoinflammatory disorders (SAID) share many clinical manifestations, albeit with variable patterns, intensity and frequency. A common definition of disease activity would be rational and useful in the management of these lifelong diseases. Moreover, standardised disease activity scores are required for the assessment of new therapies in constant development. The aim of this study was to develop preliminary activity scores for familial Mediterranean fever, mevalonate kinase deficiency, tumour necrosis factor receptor-1-associated periodic syndrome and cryopyrin-associated periodic syndromes (CAPS).