Pulmonary exacerbations in patients with primary ciliary dyskinesia: an expert consensus definition for use in clinical trials

Lucas, Jane; Gahleitner, Florian; Amorim, Adelina; Boon, Mieke; Brown, Philippa; Constant, Carolina; Cook, Simon; Crowley, Suzanne; Destouches, Damien; Eber, Ernst; Mussaffi, Huda; Haarman, Eric; Harris, Amanda; Koerner-Rettberg, Cordula; Kuehni, Claudia; Latzin, Philipp; Loebinger, Michael; Lorent, Natalie; Maitre, Bernard; Moreno-Galdo, Antonio; Nielsen, Kim; Ozcelik, HAYRİYE; Philipsen, Lue; Pohunek, Petr; Polverino, Eva; Rademacher, Jessica; Robinson, Phil; Snijders, Deborah; Yiallouros, Panayiotis; Carr, Siobhan

doi:10.1183/23120541.00147-2018

Pulmonary exacerbations in patients with primary ciliary dyskinesia: an expert consensus definition for use in clinical trials

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Lucas J. S., Gahleitner F., Amorim A., Boon M., Brown P., Constant C., ...More

ERJ OPEN RESEARCH, vol.5, no.1, 2019 (SCI-Expanded)

Publication Type: Article / Article
Volume: 5 Issue: 1
Publication Date: 2019
Doi Number: 10.1183/23120541.00147-2018
Journal Name: ERJ OPEN RESEARCH
Journal Indexes: Science Citation Index Expanded (SCI-EXPANDED), Scopus
Hacettepe University Affiliated: Yes

Abstract

Pulmonary exacerbations are a cause of significant morbidity in patients with primary ciliary dyskinesia (PCD) and are frequently used as an outcome measure in clinical research into chronic lung diseases. So far, there has been no consensus on the definition of pulmonary exacerbations in PCD.