Classification criteria for autoinflammatory recurrent fevers


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Gattorno M., Hofer M., Federici S., Vanoni F., Bovis F., Aksentijevich I., ...More

ANNALS OF THE RHEUMATIC DISEASES, vol.78, no.8, pp.1025-1032, 2019 (SCI-Expanded) identifier identifier identifier

Abstract

Background Different diagnostic and classification criteria are available for hereditary recurrent fevers (HRF)-familial Mediterranean fever (FMF), tumour necrosis factor receptor-associated periodic fever syndrome (TRAPS), mevalonate kinase deficiency (MKD) and cryopyrin-associated periodic syndromes (CAPS)-and for the non-hereditary, periodic fever, aphthosis, pharyngitis and adenitis (PFAPA). We aimed to develop and validate new evidence-based classification criteria for HRF/PFAPA.