Development of the autoinflammatory disease damage index (ADDI)


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Ter Haar N. M., Annink K. V., Al-Mayouf S. M., Amaryan G., Anton J., Barron K. S., ...Daha Fazla

ANNALS OF THE RHEUMATIC DISEASES, cilt.76, sa.5, 2017 (SCI-Expanded) identifier identifier identifier

Özet

Objectives Autoinflammatory diseases cause systemic inflammation that can result in damage to multiple organs. A validated instrument is essential to quantify damage in individual patients and to compare disease outcomes in clinical studies. Currently, there is no such tool. Our objective was to develop a common autoinflammatory disease damage index (ADDI) for familial Mediterranean fever, cryopyrin-associated periodic syndromes, tumour necrosis factor receptor-associated periodic fever syndrome and mevalonate kinase deficiency.