Development of the autoinflammatory disease damage index (ADDI)

Ter Haar N. M. , Annink K. V. , Al-Mayouf S. M. , Amaryan G., Anton J., Barron K. S. , ...Daha Fazla

ANNALS OF THE RHEUMATIC DISEASES, cilt.76, sa.5, 2017 (SCI İndekslerine Giren Dergi) identifier identifier identifier


Objectives Autoinflammatory diseases cause systemic inflammation that can result in damage to multiple organs. A validated instrument is essential to quantify damage in individual patients and to compare disease outcomes in clinical studies. Currently, there is no such tool. Our objective was to develop a common autoinflammatory disease damage index (ADDI) for familial Mediterranean fever, cryopyrin-associated periodic syndromes, tumour necrosis factor receptor-associated periodic fever syndrome and mevalonate kinase deficiency.