Development of the autoinflammatory disease damage index (ADDI)

Ter Haar N. M. , Annink K. V. , Al-Mayouf S. M. , Amaryan G., Anton J., Barron K. S. , ...Daha Fazla

ANNALS OF THE RHEUMATIC DISEASES, cilt.76, 2017 (SCI İndekslerine Giren Dergi) identifier identifier identifier


Objectives Autoinflammatory diseases cause systemic inflammation that can result in damage to multiple organs. A validated instrument is essential to quantify damage in individual patients and to compare disease outcomes in clinical studies. Currently, there is no such tool. Our objective was to develop a common autoinflammatory disease damage index (ADDI) for familial Mediterranean fever, cryopyrin-associated periodic syndromes, tumour necrosis factor receptor-associated periodic fever syndrome and mevalonate kinase deficiency.