Intraosseous pseudotumor in a child with hypofibrinogenemia

ÖZCAN H. N., ERGEN F. B., AYDINGÖZ Ü.

PEDIATRIC RADIOLOGY, cilt.44, sa.11, ss.1458-1461, 2014 (SCI-Expanded) identifier identifier identifier

  • Yayın Türü: Makale / Tam Makale
  • Cilt numarası: 44 Sayı: 11
  • Basım Tarihi: 2014
  • Doi Numarası: 10.1007/s00247-014-3004-2
  • Dergi Adı: PEDIATRIC RADIOLOGY
  • Derginin Tarandığı İndeksler: Science Citation Index Expanded (SCI-EXPANDED), Scopus
  • Sayfa Sayıları: ss.1458-1461
  • Hacettepe Üniversitesi Adresli: Evet

Özet

Intraosseous pseudotumor (i.e. chronic, encapsulated, hemorrhagic fluid collection that can be seen in any portion of the tubular bones) is an uncommon complication of severe hemophilia; however, it can occur with other rare bleeding disorders. We present the case of an 11-year-old girl with hypofibrinogenemia who had multiple intramedullary lesions that were consistent with intramedullary pseudotumor associated with this rare bleeding disorder. Percutaneous biopsy of a pseudotumor is contraindicated due to the high prevalence of complications, including life-threatening bleeding. Therefore, radiologists should make the diagnosis with characteristic MR imaging findings in a patient with a severe coagulation disorder.