Giant Lymphadenopathy Infiltrated by Gaucher Cells Mimicking Lymphoma

Yagci B., Salor O., YALÇIN B., Guerakan F., Guecer S., Bueyuepamukcu M.

PEDIATRIC BLOOD & CANCER, cilt.52, sa.7, ss.870-871, 2009 (SCI-Expanded) identifier identifier identifier

  • Yayın Türü: Makale / Tam Makale
  • Cilt numarası: 52 Sayı: 7
  • Basım Tarihi: 2009
  • Doi Numarası: 10.1002/pbc.21948
  • Dergi Adı: PEDIATRIC BLOOD & CANCER
  • Derginin Tarandığı İndeksler: Science Citation Index Expanded (SCI-EXPANDED), Scopus
  • Sayfa Sayıları: ss.870-871
  • Anahtar Kelimeler: abdominal mass, enzyme replacement therapy, Gaucher disease, lymphoma, MESENTERIC MASS, ENZYME THERAPY, DISEASE, CANCER
  • Hacettepe Üniversitesi Adresli: Evet

Özet

Gaucher disease (GD) is a lysosomal storage disease characterized by deficiency of beta-glucocerebrosidase, which results in accumulation of glucocerebroside in reticuloendothelial system, bone marrow infiltration, progressive hepatosplenomegaly, and skeletal complications. Herein we report a 5-year-old female with GD receiving enzyme replacement therapy who had giant mesenteric lymphadenopathies. Pediatr Blood Cancer 2009;52:870-871. (C) 2009 Wiley-Liss, Inc.