Primary pulmonary amyloidosis is a localized type of amyloidosis which usually presents with parenchymal nodules, diffuse alveolar damage, or submucosal deposits in the airways. Polymyozitis is an inflammatory autoimmune myopathy characterized by symmetric weakness of the limb girdle and anterior neck muscles. Nearly 80-90% of cases with polymyositis are successfully treated with steroid and cyclophosphamide combination therapies. Polymyozitis also cause secondary interstitial lung disease and the radiological findings of these two diseases may not be easily discriminated from each other. Turk J Phys Med Rehab 2072;58:159-61.