Long-term clinical course of patients with idiopathic pulmonary hemosiderosis (1979-1994): Prolonged survival with low-dose corticosteroid therapy

Kiper N., Gocmen A., ÖZÇELİK H. U., Dilber E., Anadol D.

PEDIATRIC PULMONOLOGY, vol.27, no.3, pp.180-184, 1999 (SCI-Expanded) identifier identifier identifier

  • Publication Type: Article / Article
  • Volume: 27 Issue: 3
  • Publication Date: 1999
  • Journal Name: PEDIATRIC PULMONOLOGY
  • Journal Indexes: Science Citation Index Expanded (SCI-EXPANDED), Scopus
  • Page Numbers: pp.180-184
  • Keywords: pulmonary hemosiderosis, corticosteroid, children, consanguinity, budesonide, CHLOROQUINE, CHILDREN
  • Hacettepe University Affiliated: Yes

Abstract

Idiopathic pulmonary hemosiderosis (IPH) is a rare disease of unknown etiology characterized by recurrent episodes of pulmonary symptoms such as cough,hemoptysis; and dyspnea. Our study consisted of 23 patients: 12 males and 11 females with IPH. The diagnosis was based on history, presence of anemia, and characteristic chest X-ray, and was confirmed by showing macrophages laden with hemosiderin in gastric washings or bronchoalveolar ravage and/or open lung biopsy. All but one patient were diagnosed in our department between 1979-1994,