Clinical features of childhood granulomatosis with polyangiitis (wegener's granulomatosis)

Bohm, Marek; Fernandez, Maria; ÖZEN, SEZA; Pistorio, Angela; Dolezalova, Pavla; Brogan, Paul; Barbano, Giancarlo; Sengler, Claudia; Klein-Gitelman, Marisa; Quartier, Pierre; Fasth, Anders; Herlin, Troels; Terreri, Maria; Nielsen, Susan; van Rossum, Marion; Avcin, Tadej; Rodolfo Castell, Esteban; Foeldvari, Ivan; Foell, Dirk; Kondi, Anuela; Kone-Paut, Isabelle; Kuester, Rolf-Michael; Michels, Hartmut; Wulffraat, Nico; Ben Amer, Halima; Malattia, Clara; Martini, Alberto; Ruperto, Nicolino

doi:10.1186/1546-0096-12-18

Clinical features of childhood granulomatosis with polyangiitis (wegener's granulomatosis)

Bohm M., Fernandez M. I. G., ÖZEN S., Pistorio A., Dolezalova P., Brogan P., ...More

PEDIATRIC RHEUMATOLOGY, vol.12, 2014 (SCI-Expanded, Scopus)

Publication Type: Article / Article
Volume: 12
Publication Date: 2014
Doi Number: 10.1186/1546-0096-12-18
Journal Name: PEDIATRIC RHEUMATOLOGY
Journal Indexes: Science Citation Index Expanded (SCI-EXPANDED), Scopus
Open Archive Collection: AVESIS Open Access Collection
Hacettepe University Affiliated: Yes

Abstract

Background: Granulomatosis with polyangiitis (GPA), formerly known as Wegener's granulomatosis (WG), belongs to the group of ANCA-associated necrotizing vasculitides. This study describes the clinical picture of the disease in a large cohort of GPA paediatric patients.