Papillary intralymphatic angioendothelioma: An extremely rare tumor

Creative Commons License

KAPLAN G. O., Ozdemir F. D. M., ORHAN D., AKSU A. E., Ozgur F.

JOINT DISEASES AND RELATED SURGERY, vol.32, no.1, pp.245-248, 2021 (SCI-Expanded) identifier identifier identifier identifier

  • Publication Type: Article / Article
  • Volume: 32 Issue: 1
  • Publication Date: 2021
  • Doi Number: 10.5606/ehc.2021.78112
  • Journal Name: JOINT DISEASES AND RELATED SURGERY
  • Journal Indexes: Science Citation Index Expanded (SCI-EXPANDED), Scopus, TR DİZİN (ULAKBİM)
  • Page Numbers: pp.245-248
  • Hacettepe University Affiliated: Yes

Abstract

Papillary intralymphatic angioendothelioma (PILA), an intralymphatic lesion of vascular ducts, is an extremely rare tumor. It is generally encountered as an unexpected pathology following excision of a vascular skin lesion. Re-excision is the commonly preferred treatment option once the pathological diagnosis is established. In this article, we present a 12-year-old male patient with a PILA treated with re-excision, skin grafting, and sentinel lymph node biopsy. The patient was symptom-free at annual follow-up. A sentinel lymph node biopsy during re-excision might be a good option in the surgical management of PILA. Frequent examination of lymph nodes and skin lesion also might be beneficial during the follow-ups.