Atıf İçin Kopyala
GÜLHAN B., Ozcelik U., Gurakan F., Gucer S., ORHAN D., Cinel G., ...Daha Fazla
RESPIRATORY MEDICINE, cilt.106, sa.9, ss.1278-1285, 2012 (SCI-Expanded)
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Yayın Türü:
Makale / Tam Makale
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Cilt numarası:
106
Sayı:
9
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Basım Tarihi:
2012
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Doi Numarası:
10.1016/j.rmed.2012.06.014
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Dergi Adı:
RESPIRATORY MEDICINE
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Derginin Tarandığı İndeksler:
Science Citation Index Expanded (SCI-EXPANDED), Scopus
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Sayfa Sayıları:
ss.1278-1285
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Anahtar Kelimeler:
Niemann Pick disease, Gaucher disease, Lung involvement, Bronchial cast, Flexible bronchoscopy, DEFICIENT MOUSE MODEL, PULMONARY INVOLVEMENT, NATURAL-HISTORY, B DISEASE, LAVAGE, CT
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Hacettepe Üniversitesi Adresli:
Evet
Özet
Background: Niemann-Pick disease (NPD) and Gaucher disease (GD) are well-known lysosomal storage diseases. Respiratory system involvement is an important cause of morbidity and mortality in patients with NPD and GD.