Research Information System
Journal of International Advanced Otology, vol.22, no.1, pp.1-5, 2026 (SCI-Expanded, Scopus)
Cogan’s syndrome (CS) is a rare autoimmune disorder that can cause profound sensorineural hearing loss by affecting the eyes and inner ears. A case report of a 12-year-old patient with CS who underwent successful cochlear implantation is presented. The patient developed bilateral hearing loss after a COVID-19 infection and showed no improvement with multiple medical therapies. Radiological evaluation revealed round window ossification and decreased fluid intensity in the cochlea and vestibule, consistent with inner ear inflammation and early-stage ossification. Following bilateral simultaneous cochlear implant surgery, the patient exhibited a notable improvement in auditory perception scores immediately after activation. The open-set sentence recognition performance increased from 0% to 93% 3 months after cochlear implantation. This case underscores the potential role of COVID-19 as a trigger for CS and highlights the remarkable efficacy of cochlear implants in rehabilitating hearing loss in pediatric patients with this syndrome.