Bilateral Pulmonary Langerhans's Cell Histiocytosis is Surgical Challenge in Children: A Case Report


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SOYER T., ÖZYÜKSEL G., BOYBEYİ TÜRER Ö., ÇAKMAKKAYA K., YAVUZ S., YALÇIN B., ...More

EUROPEAN JOURNAL OF PEDIATRIC SURGERY REPORTS, vol.7, no.1, 2019 (ESCI) identifier identifier

  • Publication Type: Article / Article
  • Volume: 7 Issue: 1
  • Publication Date: 2019
  • Doi Number: 10.1055/s-0039-1688771
  • Journal Name: EUROPEAN JOURNAL OF PEDIATRIC SURGERY REPORTS
  • Journal Indexes: Emerging Sources Citation Index (ESCI)
  • Keywords: pulmonary Langerhans's cell histiocytosis, children, bilateral, LUNG TRANSPLANTATION
  • Hacettepe University Affiliated: Yes

Abstract

Background Pulmonary Langerhans's cell histiocytosis (PLCH) is a rare cause of interstitial lung disease in children and more than half of the cases are bilateral. Persistent respiratory distress due to spontaneous pneumothorax (SP) in bilateral PLCH may refractory to conservative treatment and posed a great challenge to surgical modalities. A 3-year-old boy with SP due to bilateral PLCH is presented to discuss the surgical options of recurrent and refractory PLCH cases in children.