Primary myxoma of the lung is extremely rare. In this report, we present a 36-year-old man who presented to our clinic with cough and hemoptysis. His chest CT revealed a 15 x 14 mm mass with mildly spiculated borders in the right upper lobe. A wedge resection was performed under video-assisted thoracoscopy. Histologically, the tumor was diagnosed as primary pulmonary myxoma.