Congenital absence of the portal vein associated with congenital hepatic fibrosis

Gocmen R., Akhan O., Talim B.

PEDIATRIC RADIOLOGY, cilt.37, sa.9, ss.920-924, 2007 (SCI-Expanded) identifier identifier identifier

  • Yayın Türü: Makale / Tam Makale
  • Cilt numarası: 37 Sayı: 9
  • Basım Tarihi: 2007
  • Doi Numarası: 10.1007/s00247-007-0533-y
  • Dergi Adı: PEDIATRIC RADIOLOGY
  • Derginin Tarandığı İndeksler: Science Citation Index Expanded (SCI-EXPANDED), Scopus
  • Sayfa Sayıları: ss.920-924
  • Hacettepe Üniversitesi Adresli: Evet

Özet

The radiological features of a 7-year-old boy with congenital absence of the portal vein, pathologically proven congenital hepatic fibrosis, double inferior vena cava, ventricular septal defect, vertebral anomalies, crossed fused renal ectopia, and facial anomalies with pathological correlation are reported. This association between congenital absence of the portal vein and congenital hepatic fibrosis is unique.