A rare vascular malformation, Klippel-Trenaunay syndrome. Report of a case with deep vein agenesis and review of the literature

DOĞAN R., Faruk Doǧan Ö., Öç M., AKATA D., GÜMÜŞ B., Balkanci F.

Journal of Cardiovascular Surgery, vol.44, no.1, pp.95-100, 2003 (SCI-Expanded) identifier identifier

  • Publication Type: Article / Article
  • Volume: 44 Issue: 1
  • Publication Date: 2003
  • Journal Name: Journal of Cardiovascular Surgery
  • Journal Indexes: Science Citation Index Expanded (SCI-EXPANDED), Scopus
  • Page Numbers: pp.95-100
  • Keywords: Arteriovenous malformations, Klippel-Trenaunay Waber syndrome, diagnosis, Leg ulcer
  • Hacettepe University Affiliated: Yes


The Klippel-Trenaunay sydrome (KTS) is a rare anomaly characterized by naevus, soft tissue hypertrophy and varicosities which is mainly unknown etiology. Associated deep venous system abnormalities have been reported with KTS. Here, a 4-year-old-boy with KTS was reported, because of the associated popliteal vein, common femoral vein with its deep and superficial branches, and external iliac vein agenesis. The originality of the presented case is that we have never observed such a case before.