A rare vascular malformation, Klippel-Trenaunay syndrome. Report of a case with deep vein agenesis and review of the literature

DOĞAN R., Faruk Doǧan Ö., Öç M., AKATA D., GÜMÜŞ B., Balkanci F.

Journal of Cardiovascular Surgery, cilt.44, sa.1, ss.95-100, 2003 (SCI-Expanded) identifier identifier

  • Yayın Türü: Makale / Tam Makale
  • Cilt numarası: 44 Sayı: 1
  • Basım Tarihi: 2003
  • Dergi Adı: Journal of Cardiovascular Surgery
  • Derginin Tarandığı İndeksler: Science Citation Index Expanded (SCI-EXPANDED), Scopus
  • Sayfa Sayıları: ss.95-100
  • Anahtar Kelimeler: Arteriovenous malformations, Klippel-Trenaunay Waber syndrome, diagnosis, Leg ulcer
  • Hacettepe Üniversitesi Adresli: Evet

Özet

The Klippel-Trenaunay sydrome (KTS) is a rare anomaly characterized by naevus, soft tissue hypertrophy and varicosities which is mainly unknown etiology. Associated deep venous system abnormalities have been reported with KTS. Here, a 4-year-old-boy with KTS was reported, because of the associated popliteal vein, common femoral vein with its deep and superficial branches, and external iliac vein agenesis. The originality of the presented case is that we have never observed such a case before.